P717Genotype-phenotype correlation in left ventricular non-compaction of the myocardium
نویسندگان
چکیده
منابع مشابه
[Isolated non-compaction of left ventricular myocardium].
Noncompaction of the ventricular myocardium, also known as "spongy myocardium", is a rare congenital abnormality resulting from an arrest in the normal endomyocardial embryogenesis. The echocardiographic findings consist of multiple, prominent myocardial trabeculations and deep intratrabecular recesses in communication with the left ventricular cavity. This entity is a not well known cause of d...
متن کاملNon-compaction of the ventricular myocardium
Non-compaction of the left ventricle (LVNC) is a disorder of endomyocardial morphogenesis that results in multiple trabeculations in the left ventricular (LV) myocardium. This rare disorder is characterized by an excessively prominent trabecular meshwork and deep intratrabecular recesses. This idiopathic cardiomyopathy is characterized by an altered structure of the myocardial wall as a result ...
متن کاملStudy on the distribution characteristics of affected myocardium in non-compaction of left ventricular myocardium
Objectives: This study aims to investigate the distribution characteristics of the diseased area in non-compaction of left ventricular myocardium. Methods: In combination with the standardized myocardial segmentation of the American Heart Association, color Doppler ultrasound was used to analyze the occurrence of lesions in each segment of left ventricular walls in 21 patients with non-compacti...
متن کاملLeft Ventricular Non-Compaction
OBJECTIVES We aimed to test the diagnostic accuracy of cardiovascular magnetic resonance (CMR) imaging in distinguishing pathological left ventricular non-compaction (LVNC) from lesser degrees of trabecular layering seen in healthy volunteers and, in those with cardiomyopathies and concentric left ventricular hypertrophy, potential differential diagnoses. We hypothesized that pathological trabe...
متن کاملLeft ventricular non-compaction.
To cite: Steger CM. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013203430 DESCRIPTION In April 2011, a 13-month-old girl presented with dyspnoea, tachycardia and weight loss. Echocardiographic examination revealed a left ventricular non-compaction (LVNC), or spongy myocardium characterised by spongiform appearance of the left ventricle with deep recesses, a d...
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ژورنال
عنوان ژورنال: European Heart Journal
سال: 2017
ISSN: 0195-668X,1522-9645
DOI: 10.1093/eurheartj/ehx501.p717